Artigos
Herber S, Schwartz IV, Nalin T, Oliveira Netto CB, Camelo Junior JS, Santos ML, Ribeiro EM, Schüler-Faccini L, de Souza CF. Maple Syrup Urine Disease in Brazil: a panorama of the last two decades. J Pediatr (Rio J). 2014 Dec 12.
Heber et al., 2014
Frazier DM, Allgeier C, Homer C, Marriage BJ, Ogata B, Rohr F, Splett PL, Stembridge A, Singh RH. Nutrition management guideline for maple syrup urine disease: an evidence- and consensus-based approach. Mol Genet Metab. 2014 Jul;112(3):210-7.
Feier FH, Miura IK, Fonseca EA, Porta G, Pugliese R, Porta A, Schwartz IV, Margutti AV, Camelo JS Jr, Yamaguchi SN, Taveira AT, Candido H,Benavides M, Danesi V, Guimaraes T, Kondo M, Chapchap P, Neto JS. Successful domino liver transplantation in maple syrup urine disease using a relatd living donor. Braz J Med Biol Res. 2014 Jun;47(6):522-6.
Feier et al., 2014
Scaini G, Teodorak BP, Jeremias IC, Morais MO, Mina F, Dominguini D, Pescador B, Comim CM, Schuck PF, Ferreira GC, Quevedo J, Streck EL. Antioxidant administration prevents memory impairment in na animal modelo f maple syrup urine disease. Behav Brain Res. 2012 May 16;231(1):92-6.
Scaini G, Jeremias IC, Morais MO, Borges GD, Munhoz BP, Leffa DD, Andrade VM, Schuck PF, Ferreira GC, Streck EL. DNA damage in an animal model of maple syrup urine disease. Mol Genet Metab. 2012 Jun;106(2):169-74.
Scaini G, Mello-Santos LM, Furlanetto CB, Jeremias IC, Mina F, Schuck PF, Ferreira GC, Kist LW, Pereira TC, Bogo MR, Streck EL. Acute and chronic administration of the branched-chain amino acids decreases nerve growth factor in rathippocampus. Mol Neurobiol. 2013 Dec;48(3):581-9.
Scaini G, Jeremias GC, Furlanetto CB, Dominguini D, Comim CM, Quevedo J, Schuck PF, Ferreira GC, Streck EL. Behavioral responses in rats submitted to chronic administration of branched-chain amino acids. JIMD Rep. 2014;13:159-67.
Scaini et al., 2014
Scaini G, Comim CM, Oliveira GM, Pasquali MA, Quevedo J, Gelain DP, Moreira JC, Schuck PF, Ferreira GC, Bogo MR, Streck EL. Chronic administration of branched-chain amino acids impairs spatial memory and increases brain-derived neurotrophic factor in a rat model. J Inherit Metab Dis. 2013 Sep;36(5):721-30.
Scaini G, Morais MO, Galant LS, Vuolo F, Dall’Igna DM, Pasquali MA, Ramos VM, Gelain DP, Moreira JC, Schuck PF, Ferreira GC, Soriano FG, Dal-Pizzol F,Streck EL. Coadministration of branched-chain amino acids and lipopolysaccharide causes matrix metalloproteinaseactivation and blood-brain barrier breakdown. Mol Neurobiol. 2014 Oct;50(2):358-67.
Scaini G, de Rochi N, Jeremias IC, Deroza PF, Zugno AI, Pereira TC, Oliveira GM, Kist LW, Bogo MR, Schuck PF, Ferreira GC, Streck EL. Evaluation of acetylcholinesterase in an animal model of maple syrup urine disease. Mol Neurobiol. 2012 Apr;45(2):279-86.
